@article{oai:shinshu.repo.nii.ac.jp:00046323, author = {川原, 良美 and 横井, 由紀子 and 丸山, 歩美 and 岡藤, 範正 and 川原, 一郎 and KAWAHARA, YOSHIMI and YOKOI, YUKIKO and MARUYAMA, AYUMI and OKAFUJI, NORIMASA and KAWAHARA, ICHIRO}, issue = {1}, journal = {松本歯学, Journal of the Matsumoto Dental University Society}, month = {Sep}, note = {Klippel-Trenaunay-Weber syndrome (KTWS) is a rare syndrome characterized by three symptoms: hypertrophy of bones and soft tissues of limbs, varicose veins, and capillary malformation (CM). It is generally considered to be a unilateral disease that does not include the maxillofacial region, but there is also a report that unilateral hypertrophy similar to that of the extremities occurred in the maxillofacial region.In this case report, we examined the morphological characteristics of the maxillofacial skeleton from the materials for orthodontic treatment of two patients diagnosed with KTWS. In both patients, a large laterality was observed in the maxillofacial skeleton, and a congenital lack of the second premolar of the mandible was confirmed. In addition to this syndrome, there are reports of congenital absent mandibular second premolars associated with KTWS, suggesting that KTWS may be characterized by morphological laterality in the maxillofacial skeleton and symptoms with congenital absence of teeth., application/pdf}, pages = {58--66}, title = {Kippel-Trenaunay-Weber syndrome2症例の顎顔面頭蓋の歯科矯正的特徴}, volume = {47}, year = {2021} }